Ramazan Karg›n, Mustafa Akcakoyun, Soe Mao Aung, Nihal Ozdemir, Yunus Emiroglu

Keywords: Arrhythmogenic Right Ventricular Dysplasia, Bicuspid Aortic Valve.


A 22-year old boy was diagnosed arrhythmogenic right ventricular dysplasia (ARVD) with bicuspid aortic valve (BAV) after a symptomatic event of ventricular tachycardia originating from the right ventricle. Cardiac magnetic resonance imaging disclosed right ventricular enlargement, diffuse thinning of lateral wall and normal left ventricle. Echocardiography showed globally thinned, moderately enlarged right ventricle and bicuspid aortic valve. Cardiovascular malformations may be present with bicuspid aortic valve. Here we would like to report the first ARVD case with an accompanying BAV.