Osman Yılmaz, Ömer Kılıç, Nilay Hakan

Keywords: Double-outlet left ventricle, d- transposition of the great arteries, tricuspid atresia, hypoplastic right ventricle


Double outlet left ventricle is very rare congenital cardiac anomaly with numerous anatomical subtypes. Here, we presented and discussed a 2-day-old male baby with aorta and pulmonary artery arising from the left ventricle. Congenital heart disease anomalies observed in our patient included a well-developed pulmonary artery being posterior and to the left of the aorta, the aorta being anterior and to the right of the pulmonary artery (D-transposition of the great vessels), ostium secundum atrial septal defect, tricuspid artesia, severe hypoplastic right ventricle, subaortic ventricular septal defect, increased pulmonary artery blood flow with normal pulmonary artery pressure and mitral-pulmonary fibrous continuity.