Babürhan Özbek1, Kenan Öztürker2, Fatih Tomrukçu1, Kenan Abdurrahman Kara1, Ömer Faruk Şavluk3, Deniz Çevirme2, Eylem Tunçer1, Nihat Çine1, Hakan Ceyran1

1Kartal Koşuyolu Yüksek İhtisas Eğitim Ve Araştırma Hastanesi, Çocuk Kalp Damar Cerrahisi Kliniği, İstanbul, Turkey
2Kartal Koşuyolu Yüksek İhtisas Eğitim Ve Araştırma Hastanesi, Kalp Damar Cerrahisi, İstanbul, Turkey
3Kartal Koşuyolu Yüksek İhtisas Eğitim Ve Araştırma Hastanesi, Anestezi Ve Reanimasyon, İstanbul, Turkey

Keywords: Cone reconstruction, Ebstein anomaly, One and a half ventricle repair

Abstract

Ebstein anomaly is a rare pathology among congenital cardiac diseases with a prevalance of 0.5%. Ebstein anomaly patients suffer from arrhytmia, severe right ventricular dysfunction and left ventricular dysfunction due to cyanosis and right ventricular involvement. Most of the patients are presented at infancy, childhood and rarely after adolescence ages. Biventricular repair has a high mortality and morbidity and unacceptable functional results in ebstein anomaly patients with severe right ventricular dysfunction, one and a half ventricle repair yields better results. In our case, we presented a one and a half ventricle repair with a successful Cone type repair in a 34 year old male patient who referred to our clinic with cardiac arrest presentation and was detected to have functional type C Ebstein anomaly.